Malformasi Anorektal. Anorectal malformations comprise a wide spectrum of diseases, which can affect boys and girls, and involve the distal anus and rectum as well as the urinary. Anorectal malformations (ARMs) are among the more frequent congenital anomalies encountered in paediatric surgery, with an estimated incidence ranging.

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Once the constipation is managed, they mmalformasi continent. The babies are kept in the genupectoral position for 3 min by holding their facedown with hips flexed.

Physical and psychological stress to the parents, child and surgeon are less. The early management of a newborn with an anorectal anomaly is crucial.

A hemisacrum is always associated with a presacral mass, which is commonly formed of dermoids, teratomas, or anterior meningoceles.

Imperforate rectum; a new surgical technique. Etiology Anorectal malformations ARM represent a spectrum of abnormalities ranging from mild anal anomalies to complex cloacal malformations. The perineal body, that area where the fistula was located, is repaired with a few long-term absorbable sutures [ 7 ]. In males, the perineum may exhibit other features that help in recognition of this defect, such as a prominent midline skin bridge known as ‘bucket handle’ or a subepithelial midline raphe fistula that looks like a black ribbon because it is full of meconium.

The origin of the problem of constipation is unknown.


Newborns with severe anatomical malformations with associated anomalies, long duration hospital malfformasi and multiple surgical interventions may negatively influence growth and development anorketal the first 2 years of life. The only way to definitively determine the patient’s anorectal defect is to perform a distal colostogram, which of course requires the presence of a colostomy. This is also true for female patients, not including the cloaca group. This misconception has important therapeutic implications that will be discussed below.

Gross abdominal distension, sepsis, or single opening persistent cloaca warrants a diversion colostomy. The most common anomaly in females is a rectovestibular and shows a normal urethra, normal vagina, and another orifice, which is the rectal fistula in the vestibule. Am J Hum Genet. Complex vaginal mobilizations are often required and frequenly a vaginal replacement with small intestine or colon is necessary.

The other implication of missing the diagnosis of cloaca involves repairing only the rectal component of the anomaly, leaving the patient with a persistent urogenital sinus.

Increased heritability of certain types of anorectal malformations. Urinary control varies based on the length of the common channel.

Anorectal malformations

Anorectal malformations, cloaca, continence, imperforate anus. It consists of enemas, colonic irrigation, or daily suppositories to keep the rectum vacant. Perineal fistula Perineal fistulas in both male and female have traditionally been called “low” defects. During that time, sensation and voluntary muscle structures are almost not necessary because the stool, if it is solid, remains inside the colon.


See Orphanet J Anoeektal Dis.

Malformasi Anorektal | Lokananta | Jurnal Kedokteran Meditek

Nil Conflict of Interest: Bowel motility Perhaps the most important factor in fecal continence is bowel motility; however, the impact of motility has been kalformasi underestimated. Orphanet J Rare Dis. This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3. Anorectal malformations are congenital anomalies that occur in approximately 1 in live births. The etiology of such malformations remains unclear and is likely multifactorial.

Growth and development until 5years malfformasi age.

The injection is continued until the child voids, and pictures are taken during micturition in order to show, in a single picture, the sacrum, height of the rectum, perineum, malformsi location, bladder, vesicoureteral reflux if present, and urethra. Bowel management for fecal incontinence in patients with anorectal malformations. Decision-making for male newborns Male newborns with recto-perineal fistula do not need a colostomy.

Sexual problems in male patients older than 20 years with anorectal malformations. Patients with rectoprostatic fistulas have almost equal chance of having voluntary bowel movements or being incontinent.